Definition:
Elevation of intraocular pressure resulting from abnormal development of the angle of the anterior chamber

Synonym – Buphthalmos

The soft ocular tissues of infancy respond to an elevated pressure by expanding.  This results in an enlarged eye. 

congenital galucoma

 Aetiology
Anomalous development of the angle of the anterior chamber.  It may be associated with other abnormalities of the eye e.g. ANIRIDIA; Sturge Weber Syndrome- portwine stain

aniridiabuphthalmos 01

 Symptoms  
- photophobia

Signs         
- enlarged corneal diameter

Complications  
- reduced vision occurs due to corneal changes or to optic atrophy
- Delay in recognition results in permanent corneal changes and loss of vision.

Management  
- Surgical

Note:               - Beware of photophobia in an infant!